Original Guan Ying Zhang Peng Du Dapeng Fiona Fang

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This article is the original manuscript of Fiona Fang magazine.

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He looks unremarkable, dark-skinned, lean, and doesn’t talk much. He looks older than his actual age and doesn’t look like a "post-80 s", but when he talks about acrobatics, he seems to be a different person, and his words suddenly increase, and his eyes suddenly have light.

This is the prosecutor’s first impression of Yan Youlu. Based on this impression, it is really hard to imagine that he is a criminal suspect who illegally organized a number of foreigners to sneak into China for acrobatic training and performance. However, with the in-depth handling of the case, the prosecutor found that the reason why Yan Youlu embarked on the road of crime was not only related to his personal and family, but also to the inheritance of the whole Qiuqiao acrobatics.

The bitter life of acrobatics

In June 2021, the police in Huai ‘an District, Huai ‘an City, Jiangsu Province found that there were some unidentified foreigners in the acrobatic troupe on Yanyou Road, Crystal Village, Boli Town. Soon, Yan Youlu took the initiative to surrender.

Yan Youlu was born in Yan Jiaban, a well-known acrobatic family in Qiuqiao Town, Huai ‘an District. His father and grandfather are both in this line of work. Yan Youlu has been practicing kungfu with his parents since he was five years old, and began to perform on stage at the age of seven. In order to concentrate on practicing kungfu, he dropped out of primary school in the first grade. At that time, Yan Youlu always suffered from acrobatics, regardless of spring, summer, autumn and winter, even if he was physically injured, he persisted.

In an aerial training, Yan Youyou fell from a height of several meters and almost died. Until now, he still has an old scar several centimeters long on his neck.

When Yan Right’s father talked about this son, he couldn’t help but shed tears. He always said that Yan Right was so bitter step by step. Under the strict discipline of the family, Yan Youlu, who is quite talented in acrobatics, has gradually become the pillar of the acrobatic troupe. He performed with the acrobatic troupe all over the country and earned a hard money.

Recalling the previous experience of crisscrossing, Yan Youlu’s face showed a rare smile.

He proudly said: "At that time, most people went out by boat. As soon as the ship landed, we found a place with props on our backs, simply set up a shelf, knocked a few gongs and began to perform. After the end, the audience didn’t want to leave. "

In June 2007, Yan Youlu, who was in his early twenties, officially took over the acrobatic troupe from his father, became the head of the acrobatic troupe, and became the fourth generation of acrobatic descendants in the family. In December 2018, Yan Youlu was named as the acrobatic inheritor of the intangible cultural heritage project in Huai ‘an District.

Go abroad to recruit students.

In 2014, Yan Youlu’s colleague friend said that he had a relative who made a lot of money performing acrobatics in Myanmar. Yan Youlu, who was worried about the survival of the acrobatic industry, was very excited and had a bold idea.

At that time, the domestic acrobatic market was not very prosperous, and it was difficult to recruit acrobatic apprentices and inherit them all over the country. All acrobatic troupes were faced with the dilemma of no successor, and the existing acrobats were older. Especially in recent years, parents pay more attention to culture and education, and are reluctant to send their children to learn acrobatics. It is difficult for acrobatic troupes around the country to recruit young students to inherit their skills. In this way, acrobatic talents will inevitably be cut off, and the acrobatic troupe will face the risk of bankruptcy and dissolution. It is in the face of such a dilemma that Yan Youlu made up his mind to rush to Myanmar.

In August 2014, when Yan Youlu performed for the first time in Myanmar, he was warmly welcomed by the local people and attracted the attention of the local government. The local government quickly sent an invitation letter to Yan Youlu. The local government wants to cultivate local acrobatic talents, and Yan Youlu urgently needs young acrobatic students to support the acrobatic troupe and continue the acrobatic inheritance.

In October 2014, the two sides signed a contract for win-win cooperation. The local government recommended students aged 12 to 16, and Yan Youlu trained them to learn acrobatic skills. Soon, considering the limited local training conditions, Yan Youlu decided to take these students to Qiuqiao’s hometown, but the problem is, how to bring so many students back to China from Myanmar? Due to the special location of the China-Myanmar border, it is close to Yunnan, China, and the practice of smuggling is more common in the local area. Yan Youlu, who has a weak legal consciousness, is lucky.

Since 2016, Yan Youlu has smuggled 18 young students into the mainland from the Yunnan border without going through any entry and exit formalities. He also cooperated with other acrobatic troupes to introduce some students to acrobatic troupes in Shanxi, Henan and Sichuan.

In the investigation stage, Huai ‘an District Procuratorate intervened in the case in advance. In October 2022, the Huai ‘an District Procuratorate filed a public prosecution in the Huai ‘an District Court. With the efforts of the procuratorate, Yan Youlu returned all the illegal income of 500,000 yuan. Considering the circumstances of Yan Youlu’s surrender and voluntary confession and punishment, the prosecutor put forward sentencing suggestions for Yan Youlu to reduce the punishment.

On April 3, 2023, Huai ‘an District Court sentenced the defendant Yan Youlu to three years’ imprisonment, suspended for five years, and fined him 110,000 yuan for organizing others to cross the country (border) and stealing the country (border).

Promote the rescue work of Qiuqiao acrobatics

In handling the case, the dilemma of Qiuqiao acrobatics also attracted the attention of the procuratorate. The prosecutor felt that behind Yan’s right-wing crime, not only was his personal legal consciousness indifferent, but the occurrence of this case also had a certain relationship with the acrobatic inheritance dilemma including Qiuqiao Acrobatics.

Wuqiao in the north and Qiuqiao in the south. Qiuqiao acrobatics was born in the late 19th century. In the 1970s, Qiuqiao Acrobatics was founded and developed by Yan Youlu’s grandfather. From the beginning, a few people pushed carts around the streets, to the peak, Qiuqiao Acrobatics developed more than 50 performance groups, with more than 1,500 employees, more than 200 animals such as horses, tigers and lions, and more than 600 kinds of performances.

Their large-scale acrobatic programs have won many awards, and they have also gone abroad and become famous overseas. In 2008, Qiuqiao Town was named the "Hometown of Folk Culture and Art in China" by the then Ministry of Culture. In September 2014, Huai ‘an District was named "China Acrobatics Town" by China Acrobatics Association.

However, the glory of Qiuqiao acrobatics has finally become a thing of the past, and the development of acrobatic industry is shrinking day by day in the generation of Yan Right.

Especially in recent years, there are fewer opportunities for acrobatic performances. In order to survive, acrobats either start a sideline or change careers. Of course, the most deadly thing is that the acrobatic troupe, including Qiuqiao Acrobatics, has been unable to recruit young apprentices for many years. In September 2022, when the prosecutor came to Qiuqiao for an investigation and visit, the survival of the acrobatic troupe was already very difficult. The difficult problem faced by Yan Youlu Acrobatic Troupe is also the dilemma that the whole Qiuqiao Acrobatics cannot solve.

During the handling of this case, prosecutors have done a lot of extra-case investigation work, and realized that the acrobatic industry is not easy to survive. They also urgently hope that through handling cases and performing their duties, they can unite the efforts of social governance, promote government departments to do good deeds, contribute to the inheritance and development of Qiuqiao Acrobatics, fulfill their procuratorial responsibilities for protecting cultural diversity and cultural brands with local characteristics, and find the optimal solution for handling cases.

On October 14, 2022, Huai ‘an District Procuratorate wrote a research report on the development status of acrobatic industry in this area and submitted it to Huai ‘an District Committee and District Government, which received the attention and instructions of the district party secretary. On October 19, 2022, Huai ‘an District Procuratorate issued a procuratorial proposal to Huai ‘an District Culture, Radio, Film and Tourism Bureau, suggesting that Qiuqiao Acrobatics should be comprehensively counted as soon as possible and a database of Huai ‘an Acrobatics and Acrobatics Culture should be established. Actively seek special assistance funds; Introduce a mechanism to promote Qiuqiao acrobatics into the campus, coordinate tourism resources, and expand the performance opportunities of acrobatic groups; Strengthen support, allocate special funds, build acrobatic training and performance bases, and support and encourage and commend acrobatic innovative talents and projects; Organize and hold Huai ‘an Acrobatic Culture Festival and Acrobatic Performance Competition regularly to enhance the popularity of Qiuqiao Acrobatics.

On October 25, 2022, Huai ‘an District Procuratorate promoted the Propaganda Department of Huai ‘an District Committee to hold a symposium on the inheritance and development of Qiuqiao Acrobatics. Representatives from Huai ‘an Cultural and Broadcasting Tourism Bureau, Education and Sports Bureau, Boli Town Government and Huai ‘an Acrobatics Association discussed ideas and measures to help Qiuqiao Acrobatics innovate and develop continuously. With the joint efforts of all departments, Qiuqiao Acrobatics has entered local primary and secondary schools. Simple and easy-to-learn basic acrobatics will be included in the curriculum of campus interest classes, so that interested students can feel the charm of traditional culture from an early age.

(The people involved in the article are all pseudonyms. This article has been deleted. For more details, please pay attention to the last issue of Fiona Fang in August)

The original title of this magazine: "Acrobatic inheritors commit crimes, where will this go?"

Editor Su Chen Wang Li Design Liu Yan

Procuratorial Daily reporter Guan Guanying

Correspondent Zhang Peng Du Dapeng

Wonderful in the past

Original title: "18 people sneaked into the country from Myanmar! The reason behind it is not simple … "

Read the original text

Nowadays, consumers pay more and more attention to space when buying a car, which is worth mentioning in terms of space performance. Now let’s follow Xiaobian to see what it has done.

First of all, from the appearance, the front face of Cadillac CT4 looks simple and generous, and with the lattice grille, it looks more stable. At the same time, the headlights present an atmospheric design style, which can win the love of young people. The car is equipped with LED daytime running lights, automatic opening and closing, delayed closing and so on. Coming to the side of the car body, the size of the car body is 4760 mm * 1815 mm * 1428 mm. The car adopts dignified lines, which gives people a very solid feeling. With large-sized thick-walled tires, it gives people a very dynamic feeling. At the rear of the car, the rear of the car echoes the front of the car. The taillights give people a very simple feeling, and the unique exhaust pipe creates a good atmosphere.

Sitting in the car, Cadillac CT4 interior looks clean and avant-garde personality. With a three-spoke steering wheel, it is equipped with the functions of manual steering wheel up and down+front and rear adjustment, etc., and the palm fit is very high. Take a look at the central control, and with the 8-inch touch-sensitive LCD central control screen, the interior style is impressive and looks very cute. The dashboard and seats give people a good feeling, too. Let’s take a look. The car is equipped with a comfortable dashboard, and its shape has taken the sports route. The car uses leather seats, equipped with functions such as electric adjustment of auxiliary seat, electric adjustment of seat with memory, and seat proportion tilting, which has good support and comfort.

Cadillac CT4 is matched with automatic manual transmission (AT) gearbox, with an acceleration time of 6.9s per 100km, which has good power performance and is completely OK for daily use.

Cadillac CT4 is spacious in the back row, with a certain amount of headroom in the head and legs, which can be said to be more than enough for daily household use. In addition, the car is equipped with anti-lock braking (ABS), LED daytime running lights, brake assist (EBA/BAS, etc.), braking force distribution (EBD), traction control (ASR/TCS, etc.), main driving airbag, co-pilot airbag, side airbag curtain, front side airbag and other safety configurations.

What’s your main impression of this car after reading the whole article? The model class introduced today is the most considered class when many people buy their first car, mainly because the size of this class is moderate and the price is reasonable.

　

　　Recently, the Ministry of Public Security informed that in view of the recent obvious increase in gambling-related problems in online games, which seriously violated the legitimate rights and interests of the people, the Ministry of Public Security supervised and guided various localities to continuously detect a large number of major cases of opening casinos by using online games platforms.

　　

　　In April 2018, the Ministry of Public Security directed the public security organs in Henan, Beijing, Guangxi and other places to jointly act, successfully detected the case that the chess and card business department of Beijing Lianzhong Company used the online game platform to open a casino, and arrested 36 suspects including Qin, executive vice president of Lianzhong Company, Xu, head of the chess and card business department, Zhou, head of the big customer department, and Zhang, a "banker", and frozen more than 65 million yuan of funds involved.

　　At the end of January 2018, the Ministry of Public Security directed the public security organs in Jilin to successfully detect the case of using the "Deyou Circle" App to open a casino involving 7 provinces and 30 cities, and arrested several major suspects of an online company in Chengdu, Sichuan, involving more than one billion yuan in gambling money.

　　

　　In January 2018, the Ministry of Public Security directed the Zhejiang public security organs to destroy the casino criminal gang opened by the "797" online game platform in one fell swoop, coordinated the joint arrest of 52 suspects at home and abroad, and frozen funds of 330 million yuan. At present, there are still a number of major cases under investigation.

　　The relevant person in charge of the Ministry of Public Security said that the public security organs will continue to crack down and punish illegal gambling in accordance with the law. While cracking down on traditional gambling crimes, they will pay close attention to and dynamically analyze and judge the trend characteristics of new online gambling crimes, further enhance their precision strike capability, and resolutely destroy a number of online game gambling criminal gangs, effectively squeezing the living space of online game platforms involved in gambling activities.

　　The hardest hit area of online gambling on the platform of Dezhou Jockey Bureau

　　CCTV News broadcast a crazy online gambling investigation report on April 15th. The program exposed the gambling phenomenon in five mobile phone Texas Hold ’em app platforms, and directly organized members to gamble with eight clubs. (For details, see: online APP openly nearly 10,000 people gamble that large clubs earn millions of dollars a month! How is the gambling chain formed? After the program was broadcast, eight clubs disappeared into the network and never appeared again. Three of the five mobile phone Texas Hold ’em apps stopped operating within 24 hours of the program broadcast and have not resumed operations so far. The other two apps, Texas Jockey Board and Poker Circle Platform, continue to operate. Through nearly a month’s observation, the reporter found that online gambling behavior has become more and more fierce on these two app platforms, and more and more clubs have been opened.

　　

　　On April 15, CCTV news reported that there were clubs organizing members to gamble in the app platform of the Texas Convention Bureau. On April 17, the platform of the Texas Convention Bureau issued a notice saying that the platform abides by laws and regulations and prohibits all illegal activities carried out by the platform. At the same time, carry out self-examination and self-correction, strengthen supervision, and immediately close the club when gambling is found.

　　

　　The words in the announcement, hit the floor, are just the opposite.

　　After the announcement of the platform of Texas Convention Bureau, the reporter found that the clubs suspected of organizing members to gamble were still active on the platform. In less than a month, the reporter joined 13 clubs, all of which organized members to gamble. They are Jordan Club, Jingwumen Club, Big Banana Club, Fish Country Club, Royal Club, Squirrel No.1 Club, Huluwa Club, Soul Cloud Club, Turkey Club, Renhe Club, Flying Eagle Club and Everyday Deyou Club.

　　

　　If a club member wants to gamble in the platform of Texas Convention Bureau, he should first transfer the money to the club customer service, and the customer service will give the member an equal score. If the member makes a profit in gambling, the club will deduct 5% of the profit as a service fee and then transfer the remaining money to the member.

　　

　　These 13 clubs are divided into different rooms according to their chips. From one yuan to two yuan, up to 50 or 100 rooms, members gamble on the Internet every day, and some rooms with big chips can be regarded as gambling.

　　

　

　　

　　On May 10th, in a room of Huluwa Club, a player named as a small target made a profit of 22,100 yuan in two hours, and both players lost 10,000 yuan if they wanted to fight.

　　The club charges 5% of the players’ profit as a service fee, so is the club the winner with the most profit in online gambling? The reporter found through observation that the real winner is not the club, but the platform.

　　If players want to gamble on the platform, in addition to exchanging chips with the club, they must also buy gold coins from the platform before they can sit down and gamble. The income of gold coins is the profit of the platform, so how do you sell gold coins? About 1% of the chips bought. That is to say, if a player buys 10,000 yuan of chips, he will buy nearly 100 yuan of gold coins. Take the profit of that room as an example, the price of gold coins purchased by players is nearly 1400 yuan.

　　

　　The platform announcement of Texas Treaty Bureau said that it would carry out self-examination and self-correction, strengthen supervision, and immediately close the club if it found gambling behavior. All the 13 clubs that the reporter joined were suspected of gambling. Since the platform did not find out, the reporter gave feedback to the platform as a player.

　　On the evening of May 10th, the reporter reported that two of the clubs had gambling in the feedback column of the platform of the Texas Convention Bureau and the WeChat WeChat official account of the Texas Convention Bureau. Until the program was broadcast, the reporter didn’t get any feedback from the platform, and the two clubs continued to operate.

　　After the crazy online gambling report was broadcast on April 15th, the poker circle announced on the same day that it would carry out comprehensive rectification to prevent similar incidents from happening. The reporter then joined a club called Sea Lion Team Club and Spyker Celebrity Club. What these two clubs did was also to exchange chips for players and refund their profits.

　　Depot Circle: the safest platform in the industry

　　Depo Circle has a long-standing reputation in the online Texas Hold ’em field. The customer service of the club here told reporters that their platform is the safest club, and claimed that their backstage is strong, so players can bet with confidence.

　　The reporter added six clubs to the mobile app platform of Depo Circle, namely, Bighead Fish Club, Yongjinmen Club, Baby Tree Club, Underwater World Club, Youbo Entertainment Club and Grand Sailing Club. These six clubs are all clubs that organize members to gamble in the platform. What they do is to collect members’ money, get an equal score, deduct the service fee after the members make profits, and then transfer the money to the members.

　　Since the end of last year, eight ministries and commissions have jointly cracked down on online gambling, and local police have successively cracked down on online gambling cases. CCTV news also made special exposure on online Texas Hold ’em gambling twice in February and April this year. Under the background that the country has stepped up efforts to crack down on online gambling in China and purify the network environment, the customer service of the Golden Gate Club told reporters that the platform where the club is located is very safe.

　　Yongjinmen Club Customer Service:Boss, we are very stable and have a strong backstage. The boss is playing here, don’t worry. Is its headquarters in the United States or something? Anyway, don’t worry about this platform.

　　Since the reporter joined the Depo Circle Club, the club has sent messages to reporters almost every day, inviting reporters to gamble in their club.

　　Yongjinmen Club Customer Service:Good morning, boss. Our new alliance is called Yongjinmen, which is available at all levels and all day. Our brand awards are more generous than before. You can come and have a look if you have time.

　　The reporter began to pay attention to the phenomenon of online Texas Hold ’em gambling at the beginning of the year. The club organizes members to gamble in the platform of Texas Hold ’em app. Under normal circumstances, if the club can open 6 tables at the same time, it means that the members of the club are quite active, and this underwater world club in Depo Circle can open 66 tables at the same time, which can be said to be a giant club in the online Texas Hold ’em field.

　　Lawyer’s interpretation: Internet platform can’t stay out of the law

　　Online Texas Hold ’em gambling mainly involves three parties: players, clubs and platforms. So whether these three parties have violated the law, the reporter consulted a legal person for this.

　　In the online Texas Hold ’em world, thousands of players are playing cash games every day. Lawyers said that the gambling participants have been suspected of violating the People’s Republic of China (PRC) Public Security Administration Punishment Law, and the public security organs can impose administrative detention on the gambling participants for 5 to 15 days.

　　The club is responsible for soliciting players, organizing gambling, and drawing money from gambling funds. Lawyers said that the club’s behavior is suspected of gambling and opening casinos.

　　

　　Jiao Yang of Beijing Zhongjian Law Firm:According to the law, he may be sentenced to fixed-term imprisonment of not more than three years, and if the circumstances are serious, he may be sentenced to fixed-term imprisonment of not less than three years but not more than 10 years and fined for the crime of opening a casino or gathering people to gamble.

　　As for the online Texas Hold ’em platform, experts said that the platform knew that someone was gambling in the platform and did not stop it. At the same time, it also indirectly or directly profited from gambling, which was also suspected of constituting the crime of opening a casino. Even if the platform insists that it has no knowledge that the club operates gambling on its own platform, lawyers believe that the platform can not escape the legal accountability.

　　Jiao Yang of Beijing Zhongjian Law Firm:Because according to Article 7 of the Regulations on the Management of Mobile Internet Application Information Services, it has the obligation of active supervision and management. If it does not take the initiative to supervise and manage, it will bear corresponding legal responsibilities. If it does not actively supervise and manage this information, which indirectly leads to some people using its mobile Internet to provide the crime of suspected casino opening, then the corresponding network service platform is also suspected of joint crime by inaction.

　　CCTV News:On January 21, the State Council held a press conference on business work and operation in 2019. When answering a reporter’s question, Vice Minister of Commerce Qian Keming said that the holiday market supply is ready and will provide a strong guarantee for the people to celebrate the Spring Festival. Commercial departments at all levels actively take measures to increase market supply, optimize holiday services, plan and organize activities to promote consumption during holidays, and make full preparations. Mainly in the following four aspects:

　　There are plenty of holiday goods.In order to effectively increase the supply of meat in the market, the Ministry of Commerce, together with relevant departments, has formulated a plan for the delivery of two sections of reserve meat, and instructed local authorities to strengthen the delivery of reserve meat. Since mid-December last year, 177,000 tons of frozen pork have been put into the central reserve, 2,000 tons of frozen beef and mutton have been put into Qinghai, Ningxia, Tibet, Xinjiang, Gansu and other ethnic minority areas, and more than 120,000 tons of pork have been put into the local reserve. Strengthen the organization of goods supply and the connection between production and marketing, and improve the ability of ensuring supply in the holiday market. Beijing organized 46 large-scale agricultural products wholesale markets and supermarket chains to carry out joint action to ensure the supply of vegetables during the holiday, and the supply of vegetables increased by about 10% during the holiday. Hebei, Jiangxi, Guizhou, Qingdao and other regions organize large-scale circulation enterprises to increase the variety and quantity of holiday stocking through the forms of "factory-yard linkage", "agricultural supermarket docking" and "wholesale-retail docking". Commercial and trade circulation enterprises actively broaden the sources of goods and increase the stocking quantity. The stocking quantity of daily necessities is more than 20% higher than usual. Meat and vegetables can meet the consumption of 5 to 7 days, and grain and oil can meet the consumption of about 20 days.

　　The service supply is abundant.Encourage and guide catering enterprises to operate normally during the Spring Festival. Guangzhou held the activity of "Spring Festival food is not closed", and 2,300 stores of 192 chain catering enterprises participated in the activity; Hotels in Hangzhou booked more than 20,000 tables for New Year’s Eve dinner, an increase of 17.7%. A number of measures have been introduced in various places to ensure the supply of holiday services. Beijing has launched a campaign to ensure the supply of domestic services, and organized domestic workers to stay in service posts by means of "returning home at the wrong peak". It is estimated that 50,000 domestic workers will stay in Beijing during the Spring Festival. Shanghai has identified 117 domestic enterprises as the backbone enterprises for domestic security during the Spring Festival, and guided more domestic workers to stay in Shanghai.

　　The promotion activities are wonderful.Focusing on new growth points such as night consumption, holiday consumption, green consumption and brand consumption, we will organize a variety of consumption promotion activities to meet the personalized and diversified consumption needs of the people. For example, Hebei held "Happy Hebei Happy Shopping", and Sichuan held "Spring Shopping Month" and "Sichuan Goods New Year Happy New Year" and other activities. Eleven experimental pedestrian streets will also play an important role during the Spring Festival, and organize various promotional activities with rich contents.

　　The price is generally stable.Before the holiday, the market of daily necessities was generally stable, and the prices of pork and vegetables rose slightly due to factors such as increased consumer demand and increased rain and snow. According to monitoring, the average wholesale prices of pork, vegetables and fruits in 100 large wholesale markets nationwide last week increased by 2.2%, 2.4% and 2.6% respectively compared with the previous week, and the increase range was within the normal range. The prices of grain, edible oil, beef and mutton were basically the same as those of the previous week, while the prices of chicken and eggs dropped by 1.5% and 3.6% respectively.

　　Hire temporary workers and college students to make accounts, mobilize the masses to "help the platform" and ask advertising companies to concoct a glamorous year-end summary … … At the end of each year, we can always see many chaos in the inspection. Half a month’s investigation by reporters found that some of the chaos in the inspection were indeed fraudulent at the grassroots level, but some were forced out by "wonderful assessments" that were too excessive, unrealistic, ungrounded, standard-willful, and improper indicators.

　　"Make it up, just like writing a novel."

　　The staff of the labor dispute mediation Committee under the judicial system in a certain place spoke out, and basically every line had to be inspected at the end of the year. "Let’s talk about a ledger. There are only two people in the commission every day, covering hundreds of thousands of people in the business circle. Just doing mediation is already thirsty. How can there be time to record them in detail?" The staff member said frankly that we simply temporarily hired a college student from the Chinese Department to help. "But how does he know what mediation you have done in a year?" "Making it up is like writing a novel."

　　Following the guidance of this staff member, the reporter pushed open the door of a small room for half a month. Under the dim light, a busy figure and mountains of materials on the table, corner and ground are particularly dazzling.

　　At 6: 30 in the winter evening, it was already dark, and the lights in a community health service center in Jiangsu were brightly lit. In the general clinic, the doctor stared at the electronic medical record; In the rehabilitation department of traditional Chinese medicine, patients in 7788 are gossiping.

　　"It’s so late, don’t go home for dinner?" The reporter talked with several middle-aged and elderly patients for half a month. "Don’t let go. The inspection team hasn’t arrived yet, and told us to stay where we are. " Someone replied.

　　While speaking, a young doctor in his thirties came out of the consulting room. "At the end of the year, the inspection team arrived at the previous point. It is true that after work hours, you can’t let the top see that the hospital is cold and clear. "

　　"Don’t really prescribe medicine, just playacting. When the comrades of the inspection team ask, say a few good words. " Aunt Chen, a retired teacher, said that since the end of the year, more and more departments have come down to inspect the work. Not only health service centers, but also community reading rooms, party member activity rooms, democratic parliamentary halls, etc. should mobilize the masses to "help the platform".

　　In interviews, I often listen to grassroots comrades complaining that many assessments are unscientific and can’t be completed without fraud. "Some places assess the working hours of grassroots volunteers and require volunteers to stand on the road, enter the park and enter the community during working hours … … Isn’t this ridiculous? "

　　A police station coordinator told a reporter who talked for half a month that at present, many police departments have launched WeChat to facilitate WeChat official account from the public security bureau down to the police station, and their attention to WeChat official account has been assessed and ranked. "Sprint at the end of the year, let’s push everyone on the street. Some people never look at it even if they pay attention. zombie fans is everywhere, and the form is greater than the content."

　　"People with a will" resort to deceit, and those who do it are tired of coping.

　　According to local party and government cadres, there are many kinds of year-end inspection and assessment indicators in various localities and departments, including practical projects for the people, party building, building a clean and honest party style, comprehensive social management, poverty alleviation, letters and visits, population and family planning, urban management, administrative examination and approval, administration according to law, and civilization index evaluation & HELIP; … There are nearly a hundred items in rough statistics.

　　These numerous acceptance tests, whether reasonable or unreasonable, have to be completed by the grass-roots departments, but they have different attitudes.

　　First, the cadres and the masses work together to change "face" into "ticket" type. The year-end appraisal, in short, is to judge "three-six-nine" according to the performance score. The assessment results often not only affect the image of the unit, but also are closely related to the support, subsidies and welfare in the coming year. Therefore, many grass-roots departments do their best to mobilize various resources, create a warm facade, and attract policy inclinations.

　　A doctor in a community health center said: "It’s really annoying to cope with the acceptance at the end of the year, but through several months’ efforts, in exchange for several million yuan of financial support next year, the people have improved their medical conditions and the medical staff have increased their income. Why not?"

　　Second, individuals take the initiative to attack, boost performance and take the shortcut of career. A civil servant in the Yangtze River Delta said frankly that leaders can’t see all the trivial and complicated work at ordinary times, and the year-end summary is a rare opportunity. Well done, soaring; If you can’t do it well, it’s useless.

　　"There must be photos of the work of going deep into the masses. If you don’t, you will pull a few people and make up a few photos; It is best to let the following people say a few words of thanks through WeChat voice. Now it is PPT. It is easy to impress the leaders by playing the local dialect on the spot. " A grass-roots civil servant told a reporter who talked for half a month, "Our leader’s year-end summary even paid an advertising company to make it and report it as a feature film. Anyway, it is public money."

　　The third is passive cooperation, not seeking merit but seeking no type. Many grassroots cadres are deeply tired of the messy year-end inspection and assessment, but because of their feelings, they can only do some packaging with a mixed mind and meet the inspection step by step. Although this "passive" unit or cadre is not active, it often takes some effort to maintain the middle level in the year-end assessment.

　　A grass-roots civil servant reported that the assessment required them to post articles on the WeChat WeChat official account of the higher authorities, and they must read a certain amount after publishing. "Don’t ask for the first place in the assessment, but you can’t let the leaders lose face, you can only ‘ Out of pocket ’ Find a ticketing company to get it. "

　　"Wonderful Examination" can’t be cured, and formalism is hard to get rid of.

　　After one year, it is very necessary for the superior to conduct a comprehensive and meticulous examination and acceptance of the subordinate units, which can not only timely understand and master the work situation in the past year, but also commend the advanced and encourage the backward, and guide the next step of sustainable development. The problem is that many assessment indicators are fixed as soon as they are patted on the head, without reasonable argumentation, and they are too much and excessive.

　　For example, all levels and departments generally have the assessment of the quantity of information instructed by leaders. "Under heavy pressure, it is often not who does a better job at the grassroots level, but who knows more leaders and who has a harder relationship." A grass-roots staff member said that in order to be "glamorous" at the end of the year, he engaged in public relations and replenishment for individual leading secretaries. "When he was high, he published three articles a week and approved three articles."

　　Some grassroots cadres bluntly said: "Many assessments are actually not to promote work, but to brush the sense of existence of higher authorities. With the gun of year-end assessment, the superior has the right to speak and there is room for rent-seeking. "

　　There are also some assessments that are arbitrary. Grassroots cadres in many places complained to reporters who talked for half a month. Some of the creation work was often put forward at the beginning of the year, and the acceptance criteria were not issued until the end of the year, which made grassroots staff have to work overtime to deal with it.

　　Taking a key project as an example, the person in charge of the propaganda department in a certain place spoke out: "It was almost November last year, and I was informed that the assessment was to be published in the central-level media. The time was too late, so I could only make friends, ask acquaintances, and groan without illness." A county-level leading cadre in Jiangsu, who did not want to be named, said that a lot of work can be done in daily life or in the middle of the month, and it is not necessary to put it off until the end of the year.

　　Party member’s attendance rate should be assessed for some meeting activities. "The attendance rate in party member must be above 80%, but the actual attendance rate in the village is generally between 60% and 70%." Some village cadres said that it was difficult for party member, who went out to do business and work in rural areas, to come back every month. In order to cope with the assessment, he had to "process" the data.

　　Many cadres and experts believe that excessive assessment is a major source of formalism at the grassroots level. To solve this problem, the key is to make a fuss about transforming government functions and deepening administrative reform, to ask more questions from the people, and to take the satisfaction of the masses as the fundamental test standard. Only in this way can we build a service-oriented government, make grassroots cadres devote themselves to serving the masses, and eradicate the formalism that is only responsible for the upper level and not the lower level. (Talk to reporter Liu Weiwei for half a month)

Suda Masaki, Masami Nagasawa, etc.

1905 movie network news A live-action film adaptation of popular comics starring Oguri Shun and directed by Y? Ichi Fukuda exposes a luxurious lineup. Suda Masaki, Kanna Hashimoto, Masami Nagasawa, Okada Masaki, Muro Tsuyoshi, Kantarou Nakamura, Yuya Yagara and Yoshizawa Ryo joined in.

　

The original author Hideaki Sorachi’s cartoon is hilarious, full of action scenes and profound human feelings. Since it was serialized in 2004, it has been loved by audiences all over the world, with a cumulative circulation of more than 50 million copies. Comics were animated on TV in 2006. In 2010, the theater version of the first feature film earned 1.07 billion yen at the box office, and in 2013, the theater version of "The Final Story of the Silver Soul: Forever Everything Room" earned 1.7 billion yen.

　

The story of the film is set in Edo, a parallel world. The rise of the forces of "Heaven and Man" from the universe and the abandonment of knives make the once prosperous warriors begin to decline. In this era, some strange men who believe in the soul of their samurai happen many stories with their partners because of coincidence.

　

In the newly published lineup, Suda Masaki plays Shimura Shinpachi, who works in the everything house run by Yinshi; Kanna Hashimoto plays the divine joy of Yato, the only one who claims to be the strongest fighting race in the universe; Masami Nagasawa plays Shimura Tae, the new eighth sister with good looks and beautiful wrists; Okada Masaki plays the childhood sweetheart and former ally Katsura Kotarou when he was a child; Outside Pingheyuan, a reliable mechanic owner when Muro Tsuyoshi starred in Silver; Kondou Isao, the director of the special police selection group who guards the security of rivers and lakes, and Hijikata Toushirou, the only sought-after man in the selection group, and Okita Sougo, who shook hands, were starred by Kantarou Nakamura, Yuya Yagara and Yoshizawa Ryo respectively.

　

Suda Masaki, who plays the new eight, said: "In the original work, such an important role, which often says’ This is how much the world needs to vomit’, has to play a lot of funny parts, so it’s horrible to think that’ this role is too important for Hideaki Sorachi to think about me’. But even so, at least I have played a lot of tucao movies before, and I will work very hard this time. "

　

On the other hand, Kanna Hashimoto, who plays the lively God Joy, will have orange hair like the original characters. Because she is a popular character, she is quite stressed. She said, "Now every day, I want to be as powerful and popular as God Joy. There are also the famous scenes of picking nostrils and spitting in God’s music. " Masami Nagasawa, who partnered with Y? Ichi Fukuda for the first time, said: "I have never played such a movie with strange facial expressions before, and I think it is great."

　

The film started shooting in July, and Oguri Shun, who plays Yin, said to the role: "A Yin will change the role image according to the people she meets and the opportunity, so there is no part that can be accurately captured, which will be more difficult. But other actors are very confident that I will play this role. Naturally, I feel that I can perform in the direction of Silvertime. "

　

It is reported that the live-action version of Silver Soul will be released in Japan in 2017.

Recently, overseas media have exposed the latest spy photos of a group of Mercedes -AMG ONE. It is reported that this car uses a lot of F1 racing technology, and it is a racing car that can be legally on the road. At present, the new car has been in the testing stage before mass production, and it will be officially released during the year. Some media speculated that its debut time would be the 2021 Munich Auto Show, which opened in September.

In terms of appearance, Mercedes -AMG ONE continues the design language of the AMG Concept One concept car released by Mercedes-Benz in 2017. From the picture, we can see that the body of Mercedes ·AMG ONE uses super exaggerated aerodynamic design. Mercedes -AMG ONE’s body is very low, and its front face is equipped with a large-sized through air intake grille. With a long and narrow headlight group with sharp eyes, the sporty temperament highlighted by the whole car is very strong. In addition, the fender and hood of the car are equipped with air outlets, while the roof and side of the car are also equipped with air inlets, and the side is equipped with multi-spoke forged wheels. The roof also has a large-sized shark fin-like part. The shape design of the tail is even more exaggerated. In addition to a raised duck tail spoiler, the rear bumper also uses an oversized diffuser, which is full of fighting atmosphere, making people know at a glance that this car is definitely not simple.

As for the interior, some media have photographed a small part before, and it can be seen that the new car is equipped with a steering wheel design similar to F1, which is full of movement, with an independent full LCD instrument and a suspended central control LCD screen, creating a strong scientific and technological atmosphere.

In terms of power, Mercedes -AMG ONE is equipped with a 1.6T turbocharged V6 engine from F1 racing car, and four motors are added to it. Although the engine displacement of this vehicle is small, with the help of the motor, the whole power system of this vehicle can produce more than 1000Ps comprehensive horsepower in generate, while the latest news from foreign media is that the power will reach 1,200 horsepower and the fastest speed can reach 350km/h..

As the top product of Mercedes-Benz high-performance supercar family, Mercedes -AMG ONE has been tested by F1 driver Hamilton before. The new car will be delivered to users this year, with a limited production of 275 vehicles at a price of 2.7 million US dollars (about 18 million RMB), which has been sold out.

After teacher Cardi B’s WAP became popular all over the world, this song of Puxi almost became the national anthem of the United States.

WAP, the full name of wet ass pussy, the whole song is that women are very active in expressing sexual pleasure, and the lyrics are staggering.

But perhaps it is because of this straightforward strength that WAP exploded last year.

Due to the epidemic situation, it has not been possible to perform on stage. On the recent Grammy stage, Teacher Ka and Ma Dongmei Megan Thee Stallion finally performed WAP for the first time in the long-awaited performance.

The whole performance was strong and hot,

But it was this sexy explosion performance that set off the latest issue of Internet Tear X,

It not only includes the discussion about male and female genitals, family incest, thongs and Puxi’s song leading to the collapse of the American empire, but also the nude photos of Trump’s wife Melania, which instantly rushed to Twitter for hot search …

Let’s start with the Grammy performance of WAP. Although both Mr. Ka and Ma Dongmei are very spicy in this performance, the lyrics are actually completely purified.

Words with sexual implications such as "bucket" and "little dangly thing" have been edited out, which makes many friends who know the lyrics of Puxi’s song thoroughly feel like cloze when watching this Grammy stage, and a word will be empty from time to time.

But even such a purified version can’t stop conservatives from criticizing this "debauchery" performance.

This time, the American conservative who rushed to the front line against Puxi was Candace Owens (Candy for short), who was famous for supporting Trump’s black women’s movement.

Remember that she is a conservative, just support Kawaguchi, this is the test center, and she will take the test later.

The night after the Grammy, Candy and another conservative political commentator fired at Mr. Ka’s "explicit" WAP performance on Fox News.

"Fundamentally speaking, we are seeing the destruction of American values and American principles, which is terrible!"

"Parents should be afraid. This is the direction that our society is moving towards. Again, we are weakening America …

We are setting up a stage to watch the United States slowly eroded, as if we were about to see the end of an empire. "

In a word, their central idea is:Song of Puxi will finish the calf for America.

Teacher Ka’s response to this national accusation is:Yeah! ! ! ! ! ! ! ! ! ! ! We’re in fox, friends! ! !

She also gave the conservative black woman who bombarded her a nickname, Candy.

"Hey, I really want to thank Sugar, my old sister for helping me promote it, and I even got on Fox News. Boy, my pipeline broadcast volume, streaming media and sales are going up."

Teacher Ka on the left and Candy on the right.

This kind of gratitude is not all. Teacher Ka is not afraid of tearing X.

She continued to jokingly respond: Wow, imagine if WAP caused the collapse of the American empire, not North Korea’s bomb threat, terrorism, racism or bad government? ! ! The song of Puxi is absolutely epoch-making! !

Xiao Tang was very unhappy after hearing this, and turned the battlefield of tearing X from Fox News to Twitter, tweeting and accusing Teacher Ka.

"You are a cancer of culture, and young black girls are being poisoned by the so-called’ power’ you are trying to package and sell to them.

You are encouraging young women to deprive themselves of their dignity … "

"Millions of young girls are watching you, and you are good at self-criticism and sense of humor.

But the worst thing for you is to be naked and bump your vagina into another woman’s vagina.

You on the Grammy stage are the worst of you.

You can grow up. @ Kadibi "

Come and go are actually saying that they were offended by the large-scale performance of Teacher Ka and Ma Dongmei, so Cardi B posted nude photos of Mrs. Trump’s Melania as a rebuttal.

"I really don’t understand, small sugar how so hate WAP? I was just inspired by the former first lady. "

The photo of Melania can be dated back to 1996, when she took some sexy photos as a model and was published in a French magazine the following year.

When Trump was running for president in 2016, some media also published this nude photo, but after Kawaguchi was elected, this photo rarely appeared.

Sugar is not Trump’s supporter. She seems to be angered in an instant when she sees Melania’s nude photos. She asks Teacher Ka:

"Why are you so obsessed with the Trump family? You are digging up a photo of our former first lady 30 years ago. She has become a better person, but you haven’t.

What you did at the Grammy was disgusting. "

What is worth mentioning here is that Teacher Ka turned out the nude photos of Melania, perhaps not because she thought there was something wrong with taking nude photos, but because she was mocking the conservative’s "two faces".

If you think WAP performance is disgusting, don’t you feel disgusting when you see such nude photos?

If you are as conservative and firm as you say, why do you only blame Puxi’s song, but keep silent about the former first lady?

Therefore, Mr. Ka is still joking and fighting back sharply.

"I have a crush on her (Melania), and she is my idol.

She made me understand that even if I perform WAP on a large scale, I will be the first lady of the United States one day!

Wait a minute. Only white women can take nude photos and show their sexual charm when they are in their thirties. Can’t I?

Wow, the United States is so unfair, and it has the face to say that it is a free country. "

The two men broke off their heads on Twitter for several hours until 9: 00 pm, when things suddenly began to take a strange turn, from the erosion of the great American empire by large-scale performances to family incest and male genitalia (? )

Teacher Ka probably went to the top in the long-term tearing of X, and directly began to shake off the suspected black history inside the other family to attack.

"Your own husband and brother are rubbing Tintin and balls against each other there. How dare you say here that two women have a vaginal hedge?"

I also posted a Twitter screenshot of Candy admitting that "the husband cheated on his brother".

After the family was involved in the X-tearing battle, the whole battle became more intense. Candy directly said: Laugh to death, this Twitter screenshot was P.

What is even worse is her next sentence, "Only one of us has a husband who can’t control his lower body."

Oh, ho! This obviously means that Mr. Ka’s husband, Offset, has cheated many times, and both sides have dragged the other’s family off the scene, and the smell of gunpowder is getting stronger and stronger.

Teacher Ka replied, "You’re right. My husband can’t control the estrus everywhere in his lower body. Your husband is playing Tintin War with your brother at your home, and you are still here with me to force him to depend on you."

At this time, two black women with explosive fighting power were already angry and threatened to sue each other.

Candy is suing Mr. Ka for libel,

Not to be outdone, Teacher Ka counterclaims Candy for slandering her and her team for posting the Twitter screenshot.

The battle was so fierce that the people who ate melons were dumbfounded, and the melon seeds in their mouths could not be eaten. Candy even left the Twitter battlefield and sent a 13-minute video on ins, explaining how she would sue Cardi B.

Teacher ka:? ? ? ? Are you going to make a full 13-minute video? If you really can’t stand the pressure, don’t mention my name at all.

Or can we just find a beach and debate Trump and Biden face to face?

Candy: I’d like us to argue in court …

Miss Ka: Are you wearing a thong?

This epic battle is in Teacher Ka’s "Are you wearing a thong?" After coming out, it stopped abruptly.

Candy probably couldn’t accept such a coquettish operation, so he didn’t reply again.

Only naked photos of Melania were left, and they were awkwardly posted on Twitter, because Twitter officials felt that Teacher Ka’s actions did not violate the rules of Twitter.

Finally, Teacher Ka herself deleted all the posts in the war of abuse, including the nude one, because she felt that her social platform was to spread happiness and convey happiness, and these X-tearing posts were too boring.

Not surprisingly, this matter will come to an end. In fact, the antipathy of conservative parties to WAP has not just begun, but has already begun since the birth of this song.

The song of Puxi swept the major rankings last year and became a global phenomenon, which was strongly opposed by many conservatives.

For example, Ben Shapiro, also a conservative political commentator, analyzed the lyrics of this song "slutty" word by word in the program.

He also said that his wife, as a gynecologist, claimed that "wet pussy" was only a sign of vaginal infection …

He was offended by this Puxi song by the naked eye. In fact, whether he read the lyrics aloud or denied the existence of WAP from the perspective of the gynecologist’s wife,

It can be regarded as a manifestation of conservative sexual repression, and it is totally unacceptable to accept the straightforward lyrics of Puxi’s song on sexual liberation.

Netizens can ignore so much, and directly play with the way he rigidly reads the lyrics of Puxi’s song on the show.

"Ben Shapiro read the lyrics aloud, and all WAP in the world dried up."

The fierce reaction of conservatives to this song has not escaped the ridicule of netizens.

"WAP is not only a hit single, but also a mysterious panacea.

It makes conservatives admit some embarrassing things, such as Ben Shapiro can’t arouse his wife’s sexual impulse, and Candy doesn’t know what the vagina is like. We really should hold a separate award ceremony for WAP. "

This song is so popular now that all kinds of discussions have been extended not only to the song itself, but also to the big debate between American conservatives and liberals.

Liberals support women’s sexual liberation conveyed in WAP songs, while some conservative netizens feel it inappropriate.

"I can assure you that a teenager who cares about Candy will be better than a teenager who cares about Kadibi."

"Kadibi has no other talent than materializing himself. If you really think that Candy makes sandwiches (for her husband) badly, but Kadibi is the peak of women’s power in front of the whole world by putting her ass between a steel pipe, then you are wrong. "

"To all the young women in the world, don’t be Kadibi, be Candice Owens!"

There will never be a day of mutual compromise in this debate between parties, because everyone has stood firm in their respective positions.

The two heroines in the center of the war are like this, as are the netizens who watch the melons and stand in line at the end.

Only Melania, who was involved for no reason and was photographed nude by po, was speechless: I am spending my birthday with my son, don’t cue!

Source：

https://www.independent.co.uk/news/world/americas/us-politics/cardi-b-wap-candace-owens-melania-trump-nude-b1818185.html

https://www.sheknows.com/entertainment/articles/2416864/melania-trump-naked-photos-cardi-b-twitter/

Cardi B comes for Melania Trump as she shares First Lady’s ‘WAP’ nude pictures

Reporter Fu Chang and intern Ren Yawen report that the last day of February every year is "International Day of Rare Diseases". On February 23rd, the Rare Diseases Branch of Guangdong Medical Association held the 2019 "International Rare Diseases Day" charity clinic in Guangzhou Hero Square. Experts said that many patients with rare diseases still face problems such as high drug costs, and the public lacks sufficient understanding of rare diseases, calling on the society to pay more attention.

Parents’ voice of children with rare diseases: it is difficult to seek medical treatment and the medicine cost is expensive.

On the morning of the 23rd, there was a light rain in Guangzhou. Although the weather is not beautiful, there are still crowds in front of the charity clinic booth in Hero Square. Many parents came to consult with their children. They frowned slightly and pulled the doctor to ask various questions, as if they had caught the "life-saving straw". In the crowd, the reporter met Mr. Deng and his 4-year-old daughter Jia Jia (a pseudonym).

Mr. Deng told reporters that it was accidental that Jia Jia was diagnosed with a rare disease. "One day, I found that Jia Jia kept blinking when playing with her mobile phone. We thought she had an eye problem, so we quickly took her to the community hospital to see a doctor." He said that as a result, after repeated examinations, ophthalmologists could do nothing about Jiajia’s illness and could not tell why. Seeing that Jia Jia’s symptoms became more and more obvious, Mr. Deng and his wife asked around and visited experts. After many referrals, in November 2017, Jia Jia was finally diagnosed with mucopolysaccharide storage disease in Guangzhou Women and Children Medical Center.

It is understood that mucopolysaccharidosis (MPS) is a rare disease with congenital metabolic abnormality, with an incidence rate of about one in 100,000. Because of the lack of lysosomal enzymes, patients can’t decompose mucopolysaccharides in the body. The accumulated mucopolysaccharides will affect the normal function of cells and destroy many organs of the body such as brain, heart valve, lung and bone. On May 11, 2018, the National Health and Wellness Committee and other five departments jointly formulated the "First List of Rare Diseases", and mucopolysaccharide storage disease was also included.　

Jia Jia, who was diagnosed with this disease, is undoubtedly unfortunate, but compared with other children with mucopolysaccharidosis, Jia Jia may be lucky. Because at the time of diagnosis, Jia Jia’s mother had been pregnant for 30 weeks with her second child, and worried that the second baby would get sick, she immediately went to the hospital for a umbilical cord blood puncture. After confirming the health of the fetus, Jia Jia and her unborn sister were successfully matched, and a bone marrow transplant was successfully performed after her mother gave birth.

"Because of early diagnosis and early treatment, Jia Jia’s current height and intellectual development are normal." Mr. Deng said that in order to help his daughter with treatment, he had previously joined a group of patients with mucopolysaccharide storage disease, many of whom were still struggling on the road of seeking medical treatment and even took many detours. "As far as I know, the average diagnosis time of patients with rare diseases is 7 years, which often misses the ideal treatment period." Mr. Deng said. The reporter also saw at the scene that some children around the age of 10 are only 1 meter tall and have obvious abnormal physical characteristics.

The reporter learned that for the treatment of mucopolysaccharide storage disease, in addition to the bone marrow transplantation surgery accepted by Jia Jia, some experts also proposed gene therapy and enzyme replacement therapy. The former is still in the state of research and development, while the latter refers to the artificial production of enzymes that patients lack and intravenous injection into patients. However, at present, this therapy has not entered the domestic market, and the drug price is expensive, with an annual cost of up to 2 million yuan, which requires lifelong medication. Without the support of medical insurance, ordinary families simply cannot afford it.

Experts appeal: Rare diseases need attention from all walks of life.

It is reported that the World Health Organization (WHO) defines rare diseases as diseases with an incidence of 0.65-1‰, and there are currently about 7,000-8,000 species in the world. "However, due to the large population base in China, rare diseases are not uncommon in terms of the number of patients." Liu Li, chairman of the Rare Diseases Branch of Guangdong Medical Association and chief physician of the Department of Genetics and Endocrinology of Guangzhou Women and Children Medical Center, said. On the occasion of the International Day of Rare Diseases, Liu Li hopes to raise the social attention of rare diseases through public welfare clinics.

She introduced that one of the difficulties in the diagnosis of rare diseases lies in parents’ insufficient understanding of rare diseases. "In real life, a sick child has not been diagnosed and other sick children have been born. This kind of thing often happens." She said that 70%-80% of rare diseases are hereditary diseases, and 70%-80% of rare diseases occur in childhood. Liu Li suggested that parents should have a clear understanding of their children’s development and pay attention to their abnormal conditions in time. If there have been rare cases in the family, prenatal diagnosis must be made before giving birth.

"Rare diseases are rare, doctors who can diagnose rare diseases are even rarer, and drugs that can treat rare diseases are even rarer." This is the true voice of parents of children such as Mr. Deng. Liu Li said that for this reason, the Rare Diseases Branch of Guangdong Medical Association goes to remote places to give academic lectures every year, so that grassroots doctors can understand rare diseases. When patients are found to be abnormal, they can also help to refer them to experts in time, so that patients can seek medical treatment and avoid detours.

She also pointed out that due to the small number of users, high research and development costs, and the lack of relevant laws and regulations in the country, pharmaceutical companies are reluctant to take the initiative to produce rare diseases, which makes it difficult and expensive for patients to buy drugs. However, this situation is gradually improving. With the release of the first batch of rare diseases catalogue in China and the recent joint notice issued by the four departments, the value-added tax policy for rare diseases drugs has been clarified, and the tax rates of some raw materials and imported drugs have been reduced, which will reduce the drug cost of more patients with rare diseases in the future. The patients also called for more drugs to be included in the medical insurance reimbursement.

[Introduction of Several Rare Diseases]

Gaucher’s disease

Gaucher’s disease is a rare monogenic disease and the most common lysosomal storage disease, which is autosomal recessive, with an incidence of about 1/50,000~1/100,000. The mutation of glucocerebrosidase gene (GBA) leads to the lack of glucocerebrosidase activity, which leads to the accumulation of glucocerebrosidase in the lysosomes of macrophages in liver, spleen, bone, lung and even brain, forming a typical storage cell, namely "Gaucher cell", which leads to pathological changes in the affected tissues and organs, and the clinical manifestations are that multiple organs are involved and gradually aggravated. Clinically, Gaucher’s disease can be divided into three types: type ⅰ (non-neuropathy type); Type Ⅱ (acute neuropathy); Type ⅲ (chronic or subacute neuropathy). Caucasians account for about 95% of Gaucher’s disease type I, while Asians account for more than 50% of Gaucher’s disease type II and III.

Patients with Gaucher’s disease are usually characterized by splenomegaly and thrombocytopenia, which are similar to the clinical symptoms of many hematological diseases. Therefore, most patients with Gaucher’s disease will initially go to the hematology department. Hematologists should conduct glucocerebrosidase activity tests to diagnose or rule out Gaucher’s disease after excluding malignant tumors and other diseases.

Gaucher’s disease is an autosomal recessive genetic disease. If the patient’s parents give birth again, the risk of their children getting sick is 25%. For the families and relatives who have given birth to Gaucher’s disease patients, genetic counseling and detection of pathogenic gene carriers should be carried out. Prenatal diagnosis is the most effective way to prevent high-risk families from giving birth to similar children again.

neonatal diabetes

Neonatal diabetes mellitus is a rare special type of diabetes mellitus, which usually refers to persistent and progressive hyperglycemia that occurs within months after birth. The incidence rate is 1/300,000~1/400,000. In the past, the etiology of this type of diabetes was unclear, and it was regarded as an early-onset type of type 1 diabetes for a long time because it needed insulin treatment.

Neonatal diabetes can occur in both men and women, and the onset age ranges from a few days to several weeks. The earliest symptoms that lead to medical treatment are unexplained polyuria and drinking water, often accompanied by feeding difficulties, weight loss or even emaciation, mild to moderate dehydration, mental drowsiness and so on. Some children were diagnosed with elevated blood sugar in routine physical examination, but delayed diagnosis may also lead to symptoms of diabetic ketoacidosis, such as vomiting, shortness of breath, listlessness and even coma. This is a serious manifestation of diabetes, which requires urgent treatment in the hospital. A few children will have motor retardation and occasional convulsions.

Most neonatal diabetes is caused by gene mutation, and the treatment and prognosis of neonatal diabetes caused by different gene mutations are different, so chromosome microarray and gene mutation detection are needed to further clarify the cause diagnosis. Neonatal diabetic children with KCNJⅡ gene and ABCC8 gene mutation can control their blood sugar better by oral sulfonylureas than by exogenous insulin injection.

glycogen storage disease

Glycogen accumulation disease is a kind of glycogen metabolism disorder disease caused by congenital enzyme deficiency, most of which are autosomal recessive inheritance (except for X-linked recessive inheritance of type VI), and its incidence rate is 1/(2 ~ 25 thousand). The process of glycogen synthesis and catabolism requires the participation of various enzymes. There are 12 types of clinical diseases caused by these enzyme defects, among which liver diseases are the main types I, III, IV, VI and VII. Type ⅱ, ⅴ and ⅶ are mainly muscle tissue damage. The common feature of these diseases is glycogen utilization disorder, which increases in liver, muscle, kidney and other tissues.

Glycogen accumulation disease type I is caused by the deficiency of glucose -6- phosphatase system in liver, kidney and other tissues, and it is the most common glycogen accumulation disease, accounting for about 25% of the total. The main manifestations are hypoglycemia, growth retardation, muscle relaxation, abdominal distension, abnormal liver function, metabolic acidosis, increased triglyceride and uric acid in blood tests, and gout and kidney calculi may occur in older children. Most children are prone to infection. Children with the above-mentioned clinical manifestations need to go to a hospital with the conditions for genetic analysis for genetic examination and definite diagnosis and disease classification.

This disease is a rare treatable disease, and diet therapy is the main treatment for glycogen storage disease. The proportions of three nutrients in total calories are: carbohydrate 60-70%, protein 10-15%, and fat < 30%. The carbohydrate is mainly raw corn flour, and raw corn starch releases glucose at a moderate speed in the body, thus maintaining the stability of blood sugar in the body for a period of time, avoiding hypoglycemia and improving metabolic abnormalities in the body. The vast majority of carbohydrates eaten by children in one day must be replaced by raw corn flour. Infant’s diet is fed continuously for 8-10 hours with nasogastric tube at night to maintain blood sugar stability and avoid fasting for more than 4 hours. Pay attention to avoid eating foods containing sucrose, fructose, lactose and galactose, such as fruits, sweets, sugary drinks and commercial products containing milk; In the aspect of fat intake, it is necessary to limit the intake of saturated fatty acids, take more units and polyunsaturated fatty acids. Blood sugar should be maintained between 3.9 and 6.7 mmol/L, so as to ensure the normal growth and development of children.

　 　　Special feature of 1905 film network The film starring Jackie Chan and a group of Hollywood stars was released in the mainland on February 19th. Although the main appeal of this film is not to restore history, the historical background is still an important part of the film. The repeated invasion of Xiongnu beyond the Great Wall, the mysterious appearance of western troops and various contradictions in the process of national integration are all problems that the Han and Yuan emperors have to face and solve after they acceded to the throne. On the whole, the film’s "entertainment adaptation" of history is well-founded.

　 　　In this film, Jackie Chan plays a Han Dynasty general named Huo An. He meets Roman general Lucius and his small army in the Gobi Desert in the Western Regions. At that time, the border was always invaded by the Huns. Li Rengang, the director and screenwriter, then built an interesting story around three forces: the general of the Han Dynasty, the Xiongnu and the Roman army. In fact, the real history of this period is also very interesting. During the reign of Emperor Han and Yuan, Wang Zhaojun was sent to the fortress to marry the Huns, crusade against Zhi Zhi Khan, and captured a Roman army. In the west, Caesar and Pompeii clashed with each other, which led to the Roman Civil War. The result of this civil war directly laid the political, economic and cultural structure of the western world in the next 300 years.

There is a certain historical basis for the Roman army to appear on the border of China.

[The legendary disappearing army]

On the border of China, Roman troops were employed by the Han Dynasty to discuss Zhi Zhi Khan.

　 　　In the Western Han Dynasty during the Han and Yuan Dynasties, a mercenary from the Roman Republic did appear, which is probably the historical basis of the plot of Heavenly Generals and Heroes. In 53 BC, crassus, consul general of the Roman Republic, launched a war against Iran. I thought this was a quick battle, but I didn’t expect the Iranian army to panic in the Roman army and crassus was captured and beheaded. In 20 BC, Rome and Iran signed an armistice agreement. At this time, the Roman Republic asked Iran to return the captured army, but the army that broke through from the Iranian encirclement disappeared without a trace.

　 　　For many years, the whereabouts of this 6,000-strong army have been unknown. It wasn’t until 1947 that the English sinologist De Xiaoqian wrote the article "The Strike of Ancient China" that the mystery was solved. In ancient China, Liba referred to the Roman Republic. The "ancient China’s Li-ba-cheng" refers to a city inhabited by Romans that once appeared on Chinese territory. In the biography of Han Chen Tang written by Ban Gu, it is recorded that in 36 BC, a strange army appeared on the road where Chen Tang led more than 40 thousand troops to crusade against Zhi Zhi Khan. This army has "more than 100 infantry, fighting in a fish-scale array" and "guarding the city with heavy wood". According to historians’ interpretation, this defensive formation of "heavy wooden city" fortifications and fish scales with circular shields was only adopted by the Roman army. Historians reasoned that this strange army was a small force that broke through after the failure of the Roman Republic to go to Iran.

　 　　It is speculated that this unit was unable to return to China because the road was blocked by the Iranians when it broke through, so it had to turn to the plateau in Iran and wait for an opportunity to move eastward. Fortunately, they tore a hole in the lax defense line in eastern Iran and migrated to Central Asia to go to Zhizhi. Finally, they were collected by Chen Shang and brought back to China. Of course, this army was not idle after the surrender. They became Chen Tang’s "mercenaries" and made great contributions to the campaign against Zhi Zhi Khan. Later, the Emperor of the Han Dynasty issued a letter to place them at the foot of Zhaomian Mountain (now Yongchang County) in the south of Fanhe County, and put them in the county. In 592 ad. In view of the fact that Liba people have merged with Han people, Emperor Wendi of Sui Dynasty issued a letter to merge Liba County into Fanhe County. At this point, Li Ba built the county for 612 years. In this way, the Liban people in China quietly disappeared in the vicissitudes of history.

The ethnic groups on the border are extremely rich and diverse.

[The famous Silk Road]

The Western Han Dynasty was prosperous, and all ethnic groups joined Zhaojun and went out to make a good knot.

　 　 Although Kung Fu and martial arts are the selling points of "Heavenly Master", Li Rengang still set a tone of national unity and world peace for the film. On the famous "Silk Road", various nationalities gathered and blended here, which surprised the audience at the great national strength and tolerance of the Han Dynasty. The so-called Silk Road refers to the trade route in the northern part of Eurasia, which is in contrast with the ancient tea-horse road in the south. This trade route was first developed by Zhang Qian during the reign of Emperor Wu of the Western Han Dynasty. This action is called "the journey of hollowing out", and the envoys sent by Emperor Wu of the Han Dynasty reached Alexandria in Egypt as far as today. This is the farthest country reached by the official envoys of the Western Han Dynasty. In the Eastern Han Dynasty, Ban Chao extended the Silk Road again, reaching as far as Rome from Xi ‘an.

　 　 According to historical records, in the Western Han Dynasty, roughly sixteen ethnic minorities, such as Xiongnu, Donghu, Wuhuan, Xianbei, Turkic, Qidan, Rouran and Uighur, were active in the territory of China. The western Han government ensured the overall stability of these ethnic minority areas through certain means such as war, administrative regional setting, intermarriage and trade. These policies make the southwest, south China and southeast China also join the national rule. Although the control over the southern minorities at this time was far less powerful than that in Ming and Qing Dynasties, the military and political obstacles between the central plains and the southern mountainous areas were lifted, which made the south in a stable and orderly environment for a long time in the Han Dynasty and undoubtedly promoted the exchanges between the southern minorities and the central plains.

Zhaojun’s departure from the Great Wall and his relatives contributed to the peaceful coexistence of Han and Xiongnu.

　 　 When it comes to the national integration during the Han and Yuan Dynasties, we have to say that Zhaojun, who is well-known in Chinese, went to the fortress. This allusion tells the story of a maid-in-waiting named Zhaojun who pretended to be a princess of the Han Dynasty and married Uhaanyehe of the Xiongnu. It is said that Zhaojun was very beautiful and natural and graceful. Emperor Han Yuan regretted seeing such a beautiful maid-in-waiting going to marry. During his life in Xiongnu, Wang Zhaojun adapted to the lifestyle there and got along very well with the local people. She not only advised her husband to live in harmony with the Han Dynasty, but also spread the culture of the Han nationality to the Huns. It should be said that the marriage between Wang Zhaojun and Xiongnu is not only a political marriage, but also a cultural integration. Her arrival, in a sense, "assimilated" Huns. Perhaps because of her, the Han Dynasty and Xiongnu lived in harmony for 60 years. After Wang Zhaojun’s death, she was buried in Daqing Mountain controlled by Huns. The Huns built a tomb for her, and later generations called her tomb "Qingzhong" and regarded it as a fairy.

The struggle between Caesar and Pompeii is brilliantly presented in the English drama Rome.

[What happened in the Roman Empire]

There was a "great earthquake" in the Roman Republic. Caesar and Pompeii tore each other apart.

　 　 During the Han and Yuan Dynasties, the whole Han Empire basically presented a thriving scene, while the Roman Republic was not peaceful at the same time. Because of the above-mentioned "Rome was defeated by Iran", a large earthquake in the political circle of the Roman Republic was triggered. In 60 BC, crassus, Caesar and Pompeii, three politically frustrated people, formed the so-called "First Triumphal Alliance". However, these three people, strange bedfellows, have never shared common interests, and this alliance will soon be in jeopardy. After the defeat of the Iranian crusade and crassus’s beheading, the remaining contradictions between the two giants intensified. Caesar’s expedition to Gaul was successful, and he mastered a large number of troops. At the same time, he also got a lot of public support with the book "The Battle of Gaul", and with the huge wealth from Gaul, he gradually stepped onto the peak of strength and power. Under such circumstances, the Senate began to unite with Pompeii, who was left out in the cold, and began to attack Caesar and his henchmen.

　 　 In 50 BC, Pompeii and the Senate made a decision to ask Caesar to surrender his military power and return to China to serve in the following year. In a practical sense, this announced Caesar’s "demotion" and also meant a complete break between Caesar and Pompeii. Caesar, who received this decision, did not buy it. He wrote back to the Senate and Pompeii, asking Pompeii to surrender the military power, otherwise he would not obey the decision of the Senate and would not hesitate to launch a civil war to safeguard his dignity. After receiving the reply, the Senate thought that Caesar had handed in an essay, resolutely refused to follow it, and insisted on their previous decision. Caesar sent an envoy to Rome to mediate, but the envoy was persecuted by Pompeii and the Senate. Knowing this, Caesar was forced to flee to Gaul. The Senate regarded Caesar’s move as a preparation for war, so it declared Caesar a national public enemy. At this point, the civil war broke out in the Roman Republic.

　 　 The civil war in Rome opened a new page in Roman history and made Rome develop from a republic to a new stage of monarchy. When preparing for the war, Caesar carried out the policy of equal rights for residents and Romans in all provinces, which expanded his social foundation and promoted social progress. After the First World War, Rome’s political, economic and social structure became more modern and reasonable, while China would continue to be in a feudal society. Therefore, the Roman civil war that took place during the Han and Yuan Dynasties was barbaric on the surface, but in fact it was a manifestation of progress. Although the Western Han Dynasty was stable and prosperous, it accumulated many social contradictions, and various problems gradually emerged in the next hundred years, which brought even greater disasters.